Sie suchten nach: L(-)-Galactose

Artikel-Nr: (BOSSBS-7593R-CY5.5)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-7593R-CY5.5

Beschreibung: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-7593R-CY7)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-7593R-CY7

Beschreibung: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-3983R-CY7)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-3983R-CY7

Beschreibung: Galactokinase is a major enzyme for the metabolism of galactose and its deficiency causes congenital cataracts in the adult population. GALK1 sequence shares the greatest level of conservation, 44.5% identity with that from E. coli and 34.6% amino acid identity with the product of the human GALK2 gene.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-3983R)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-3983R

Beschreibung: Galactokinase is a major enzyme for the metabolism of galactose and its deficiency causes congenital cataracts in the adult population. GALK1 sequence shares the greatest level of conservation, 44.5% identity with that from E. coli and 34.6% amino acid identity with the product of the human GALK2 gene.

UOM: 1 * 100 µl

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Artikel-Nr: (MOLE16084407-1KG)

Lieferant: Molekula

Hersteller Artikel Nummer : 16084407-1KG

Beschreibung: D(+)-Galactose

UOM: 1 * 1 kg

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Artikel-Nr: (EHERC13996500)

Lieferant: EHRENSTORFER

Hersteller Artikel Nummer : C13996500

Beschreibung: D(+)-Galactose

UOM: 1 * 0,25 g

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Lieferant: Roth Carl

Beschreibung: D(+)-Galactose

Artikel-Nr: (BOSSBS-7593R-A680)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-7593R-A680

Beschreibung: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-7588R-A555)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-7588R-A555

Beschreibung: Necessary for the biosynthesis of the Pk antigen of blood histogroup P. Catalyzes the transfer of galactose to lactosylceramide and galactosylceramide. Necessary for the synthesis of the receptor for bacterial verotoxins.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-16215R-A680)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-16215R-A680

Beschreibung: Catalyses the transfer of sulfate to beta-1,3-linked galactose residues in O-linked glycoproteins. Good substrates include asialofetuin, Gal-beta-1,3-GalNAc and Gal-beta-1,3 (GlcNAc-beta-1,6)GalNAc.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-8056R)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-8056R

Beschreibung: KLHL14 is a member of the KLHL family. The kelch motif was initially discovered in Kelch. In this protein there are six copies of the motif. It has been shown for one member that it is related to Galactose Oxidase for which a structure has been solved. Two isoforms of this protein exist - 70kDa and 43kDa.

UOM: 1 * 100 µl

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Artikel-Nr: (BOSSBS-8056R-CY5)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-8056R-CY5

Beschreibung: KLHL14 is a member of the KLHL family. The kelch motif was initially discovered in Kelch. In this protein there are six copies of the motif. It has been shown for one member that it is related to Galactose Oxidase for which a structure has been solved. Two isoforms of this protein exist - 70kDa and 43kDa.

UOM: 1 * 100 µl

Sale

Artikel-Nr: (BOSSBS-7593R-A488)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-7593R-A488

Beschreibung: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

UOM: 1 * 100 µl

Sale

Artikel-Nr: (BOSSBS-7593R-FITC)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-7593R-FITC

Beschreibung: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.

UOM: 1 * 100 µl

Sale

Artikel-Nr: (BOSSBS-3983R-CY3)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-3983R-CY3

Beschreibung: Galactokinase is a major enzyme for the metabolism of galactose and its deficiency causes congenital cataracts in the adult population. GALK1 sequence shares the greatest level of conservation, 44.5% identity with that from E. coli and 34.6% amino acid identity with the product of the human GALK2 gene.

UOM: 1 * 100 µl

Sale

Artikel-Nr: (BOSSBS-3983R-CY5.5)

Lieferant: Bioss

Hersteller Artikel Nummer : BS-3983R-CY5.5

Beschreibung: Galactokinase is a major enzyme for the metabolism of galactose and its deficiency causes congenital cataracts in the adult population. GALK1 sequence shares the greatest level of conservation, 44.5% identity with that from E. coli and 34.6% amino acid identity with the product of the human GALK2 gene.

UOM: 1 * 100 µl

Sale