Anti-GORAB Rabbit Polyclonal Antibody

Lieferant: Bioss
BS-6643R
BOSSBS-6643REA 965 CHF
BOSSBS-6643R
Anti-GORAB Rabbit Polyclonal Antibody
Antikörper
Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070]; also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.

WB(1:100-1000), IHC-P(1:100-500), IF(IHC-P)(1:50-200)

Type: Primary
Antigen: SCYL1BP1
Clonality: Polyclonal
Clone:
Conjugation: Unconjugated
Epitope:
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TECHNISCHE DATEN

Antigen-Symbol GORAB
Environmentally Preferable
Antigen-Name Golgin, RAB6-interacting
Antigen-Synonyme GO|NTKLBP1|SCYL1BP1
Antikörper-Typ Primär
Klonalität Polyklonal
Konjugation Unconjugated
Reaktivität Human,Rat,Mouse
Wirt Rabbit
Gen-ID 92344
Isotyp IgG
Western blot Yes
ImmunoChemie Yes
Immunogen 190-240/394
Form liquid
Reinigung Purified by Protein A.
Konzentration 1 ug/ul
Lagerungspuffer Aqueous buffered solution containing 100ug/ml BSA, 50% glycerol and 0,09% sodium azide. Store at -20°C for 12 months.
Transporttemperatur 4 °C

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